Surgical treatment of Hirschsprung’s disease at the National Children’s .. Enfermedad de Hirschprung. Fantobal-Rojas A. Constipación crónica en el niño. La enfermedad de Hirschsprung es un trastorno congénito infrecuente (afecta aproximadamente a 1 de cada recién nacidos en EE. UU.) que provoca. El estreñimiento se debe diferenciar de la enfermedad de Hirschsprung y de alteraciones anatómicas y metabólicas. La evaluación clínica incluye una historia.

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Children referred from the surrounding Caribbean islands were referred at an older age, but their overall outcome was not worse than local Barbadian patients.

[Hirschsprung’s disease: the immunohistochemistry as ancillary method for the diagnosis.]

In reality, however, many of these factors continue to be lacking in the majority of the Caribbean isles resulting in late diagnosis and referral of children with HD. Primary versus staged pull-through for the treatment of Nips disease. However, many factors hirschsptung by Somme 8 which will affect earlier diagnosis and referral have improved and will continue to improve throughout the Caribbean.

However you have to be at the expectation of the results when the patient defecates after the surgery, because it can present fecal incontinence or constipation. Vieten D, Spicer R.

In the pediatric population a constipation history since the first month of life, the delay on the elimination of meconium beyond the 24 hours, abdominal distension is a suspicion of Congenital Megacolon. With hircshsprung to Somme’s 8 finding of using a rectal suction biopsy as a factor contributing to earlier diagnosis, we note the delay in diagnosis of some of the children who presented in the neonatal period Table 4.


Hirschsprung disease in the newborn.

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There is ample evidence that the primary pull-through procedure for HD is safe and effective in most situations, including the neonatal period 8. A developmental model and approach. The clinical presentation changes between children and adults. Long term outcome was assessed by the use of a simple questionnaire which was completed by the authors after personal dr telephone contact with patients, their parents or guardians or the referring physician.

It is thought to either occur from a failure of neuroblasts in neural crest cells to migrate into bowel segments or degeneration of already migrated neuroblasts.

Hence it is claimed that the single-stage repair is ideal for use hirschprung developing countries where access to medical care may be hampered by poor transportation and communication systems 8. The two children with Grade 1V continence were both developmentally delayed, one child having cerebral palsy sn a perinatal history of maternal pregnancy-induced hypertension and fetal distress at birth and the other having congenital hydrocephalus.

Case 6 Case 6. Three of the children had a positive family history of HD.

Enfermedad de Hirschsprung | Medicina

Constipation is a common problem in children throughout the world, and the Caribbean is encermedad exception. Currenl Problems in Surg. Yanchar NL, Soucy P. While transportation and poor communication systems may indeed be a challenge for the Caribbean, especially in the presence of multiple small islands, a number enfermedac factors make routine use of the primary pull-through procedure inappropriate for the Caribbean, if not impossible.


A very small number may present in the adult population 1. Hirschsprung disease is certainly diagnosed after birth. It is postulated that hypoganglionosis reduced number of ganglion cells handles intestinal pseudo-obstruction 4. Comparison with c1inical amI radiological criteria.

Hirschsprung disease | Radiology Reference Article |

Veinte eran varones y siete hembras. The mean age at presentation was 30 months ranging from day 1 of life to 24 years. Hence NEC in the term infant should raise dde suspicion and a rectal suction biopsy performed to exclude HD Endorectal pull-through without preliminary colostomy on neonates with Hirschsprung’s disease. There were 20 males and seven females.

The mean time to follow-up was 64 months ranging from two to months. Authors must state that they reviewed, validated and approved the manuscript’s publication. Changes in colorectal function in severe idiopathic chronic constipalion.

Mechanisms of idiopathic constipation:

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